Bietti's tapetoretinal degeneration with marginal corneal dystrophy crystalline retinopathy.

Bietti ' s tapetoretinal degeneration with marginal corneal dystrophy ( crystalline retinopathy ) : case report

A tapetoretinal degeneration combined with a marginal corneal dystrophy was described by Bietti in three patients (two of whom were brothers) in 1937.' The fundus picture was reported to be similar to that of retinitis punctata albescens, but the spots, located mainly at the posterior pole, were refractile, polygonal, and could be seen at all levels of the neuroretina. Pigment changes were seen...

Evolution of Cellular Inclusions in Bietti’s Crystalline Dystrophy

Bietti's crystalline dystrophy (BCD) consists of small, yellow-white, glistening intraretinal crystals in the posterior pole, tapetoretinal degeneration with atrophy of the retinal pigment epithelium (RPE) and "sclerosis" of the choroid; in addition, sparking yellow crystals in the superficial marginal cornea are also found in many patients. BCD is inherited as an autosomal-recessive trait (4q3...

Specular microscopic findings of corneal deposits in patients with Bietti's crystalline corneal retinal dystrophy.

Cystoid Macular Edema in Bietti's Crystalline Retinopathy

A 27-year-old man with progressive bilateral visual decline was diagnosed to have Bietti's crystalline dystrophy (BCD). Fluorescein angiography revealed bilateral petaloid type late hyperfluorescence implicating concurrent cystoid macular edema (CME). Optical coherence tomography exhibited cystoid foveal lacunas OU. During the follow-up of six years, intraretinal crystals reduced in amount but ...

Clinical findings, course, and progress of Bietti's corneal degeneration in the Dahlak islands.

Bartolucci (1933) and Zanettin (I937) reported the presence of an unusual corneal disease in Italian Somaliland and the Dahlak Islands respectively. Falcone (I 954) published an excellent detailed account based on a large sample collected over I5 years in Mogadiscio. Coinciding with his observations, Guerra in Asmara had recorded similar findings; he communicated them to Bietti in Rome, who vis...